Cardiac amyloidosis and its electrophysiologic manifestations
نویسندگان
چکیده
Amyloidosis is caused by deposition of abnormal amyloid fibrils with the feared consequence end stage organ failure. Cardiac amyloidosis (CA) an increasingly recognized antecedent cardiomyopathy. CA classified into transthyretin variants (ATTRwt – wild type and ATTRv genetic variant) a light chain variant (AL); each these can be associated unique electrophysiologic abnormalities. Pacing indications in current societal guidelines do not specify treatment options infiltrative cardiac diseases, such as CA, new disease modifying treatments are altering landscape for intervention. Given paucity data, national international groups have differing recommendations. In this review, we aim to update highlight changes seen their respective course suggest areas future
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ژورنال
عنوان ژورنال: Cardiologia Hungarica (Nyomtatott)
سال: 2022
ISSN: ['0133-5596', '1588-0230']
DOI: https://doi.org/10.26430/chungarica.2022.52.3.198